Klippel-Trenaunay syndrome is a slow-flow combined vascular anomaly.Klippel-Trénaunay-Weber Syndrome or KTS is a rare congenital medical condition in which blood vessels and/or lymph vessels fail to form properly.
Symptoms and diagnosis
* One or more distinctive port-wine stains with sharp borders
* Varicose veins
* Hypertrophy of bony and soft tissues, that may lead to local gigantism or shrinking.
* An improperly developed lymph system
Treatment
KTS is a complex syndrome, and no single treatment is applicable for everyone. Treatment is decided on a case-by-case basis with the individual's doctors.
Debulking has been the most widely used treatment for the syndrome, and has been used for decades. Progress has been made in this method over the course of the past couple decades, but it is still an invasive procedure, and has many complications. As other choices now exist for KTS patients, this method is generally reserved as a last resort.
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